Journal of Pediatric Neurosciences
CASE REPORT
Year
: 2016  |  Volume : 11  |  Issue : 4  |  Page : 373--377

Neuroblastoma presenting as opsoclonus-myoclonus: A series of six cases and review of literature


Jagdish P Meena1, Rachna Seth1, Biswaroop Chakrabarty1, Sheffali Gulati1, Sandeep Agrawala2, Priyanka Naranje3 
1 Department of Pediatrics, All Institute of Medical Sciences, New Delhi, India
2 Department of Pediatric Surgery, All Institute of Medical Sciences, New Delhi, India
3 Department of Radiodiagnosis, All Institute of Medical Sciences, New Delhi, India

Correspondence Address:
Jagdish P Meena
Department of Pediatrics, All India Institute of Medical Sciences, Room No. 3058, Teaching Block, New Delhi
India

The opsoclonus-myoclonus ataxia syndrome (OMAS) also called “Kinsbourne syndrome” or “dancing eye syndrome” is a rare but serious disorder characterized by opsoclonus, myoclonus, and ataxia, along with extreme irritability and behavioural changes. Data on its epidemiology, clinical features, and outcome are limited worldwide. The aim of the study was to evaluate the clinical profile and outcome of children with OMAS. A retrospective data of all children presented to Pediatric oncology clinic with a diagnosis of opsoclonus-myoclonus from 2013 to 2016 were collected. 6 patients with a diagnosis of OMAS were presented over a 4-year period. All 6 cases had paraneoplastic etiology. All Children had good outcome without any relapse. Paraneoplastic opsoclonus myoclonus had a good outcome in our experience.


How to cite this article:
Meena JP, Seth R, Chakrabarty B, Gulati S, Agrawala S, Naranje P. Neuroblastoma presenting as opsoclonus-myoclonus: A series of six cases and review of literature.J Pediatr Neurosci 2016;11:373-377


How to cite this URL:
Meena JP, Seth R, Chakrabarty B, Gulati S, Agrawala S, Naranje P. Neuroblastoma presenting as opsoclonus-myoclonus: A series of six cases and review of literature. J Pediatr Neurosci [serial online] 2016 [cited 2021 Jan 17 ];11:373-377
Available from: https://www.pediatricneurosciences.com/article.asp?issn=1817-1745;year=2016;volume=11;issue=4;spage=373;epage=377;aulast=Meena;type=0