Journal of Pediatric Neurosciences
CASE REPORT
Year
: 2016  |  Volume : 11  |  Issue : 3  |  Page : 237--240

Dwarf with dual spinal kyphotic deformity at the cervical and dorsal spine unassociated with odontoid hypoplasia: Surgical management


Guru Dutta Satyarthee, Dipanker Singh Mankotia 
 Department of Neurosurgery, All Institute of Medical Sciences, New Delhi, India

Correspondence Address:
Guru Dutta Satyarthee
Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi - 110 029
India

Morquio's syndrome is associated with systemic skeletal hypoplasia leading to generalized skeletal deformation. The hypoplasia of odontoid process is frequent association, which is responsible for atlantoaxial dislocation causing compressive myelopathy. However, development of sub-axial cervical kyphotic deformity unassociated with odontoid hypoplasia is extremely rare, and coexistence of dorsal kyphotic deformity is not reported in the western literature till date and represents first case. Current case is 16-year-old boy, who presented with severe kyphotic deformity of cervical spine with spastic quadriparesis. Interestingly, he also had additional asymptomatic kyphotic deformity of dorsal spine; however, odontoid proves hypoplasia was not observed. He was only symptomatic for cervical compression, accordingly surgery was planned. The patient was planned for correction of cervical kyphotic deformity under general anesthesia, underwent fourth cervical corpectomy with resection of posterior longitudinal ligament and fusion with autologous bone graft derived from right fibula, which was refashioned approximating to the width of the corpectomy size after harvesting and fixed between C3 and C5 vertebral bodies and further secured with anterior cervical plating. He tolerated surgical procedure well with improvement in power with significant reduction in spasticity. Postoperative X-ray, cervical spine revealed complete correction of kyphotic deformity cervical spine. At follow-up 6 months following surgery, he is doing well. Successful surgical correction of symptomatic cervical kyphotic deformity can be achieved utilizing anterior cervical corpectomy, autologous fibular bone graft, and anterior cervical plating.


How to cite this article:
Satyarthee GD, Mankotia DS. Dwarf with dual spinal kyphotic deformity at the cervical and dorsal spine unassociated with odontoid hypoplasia: Surgical management.J Pediatr Neurosci 2016;11:237-240


How to cite this URL:
Satyarthee GD, Mankotia DS. Dwarf with dual spinal kyphotic deformity at the cervical and dorsal spine unassociated with odontoid hypoplasia: Surgical management. J Pediatr Neurosci [serial online] 2016 [cited 2021 May 13 ];11:237-240
Available from: https://www.pediatricneurosciences.com/article.asp?issn=1817-1745;year=2016;volume=11;issue=3;spage=237;epage=240;aulast=Satyarthee;type=0