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NEUROIMAGING
Year : 2007  |  Volume : 2  |  Issue : 1  |  Page : 39-40
 

Complex split-cord malformation associated with situs inversus totalis


Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi-110029, India

Correspondence Address:
Deepak Agrawal
Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi -110029
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/1817-1745.32009

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   Abstract 

Although meningoceles are known to be associated with split cord malformations, the association of dextrocardia is extremely rare. The authors report a case of a 15 day male child who had an atretic meningocele in the lumbosacral region along with dextrocardia and a split cord malformation with a posterior spur. This importance of preoperative MRI for proper management of such patients is highlighted in this report.


Keywords: Complex split-cord malformation, posterior spur, situs inversus.


How to cite this article:
Agrawal D, Mahapatra A K. Complex split-cord malformation associated with situs inversus totalis. J Pediatr Neurosci 2007;2:39-40

How to cite this URL:
Agrawal D, Mahapatra A K. Complex split-cord malformation associated with situs inversus totalis. J Pediatr Neurosci [serial online] 2007 [cited 2020 Oct 26];2:39-40. Available from: https://www.pediatricneurosciences.com/text.asp?2007/2/1/39/32009



   Case Report and Discussion Top


A 15-day-old male child presented with swelling over the lower back since birth. Examination revealed an atretic meningocele in the lumbosacral region. There was good spontaneous movement at all joints, and bladder and bowel functions appeared to be intact. Chest radiograph revealed dextrocardia [Figure - 1], and an MRI spine revealed a small meningocele with a bony spur which was arising from the posterior elements and causing split-cord malformation [Figure - 2],[Figure - 3]. The findings were verified intraoperatively; and excision of the meningocele, removal of the bony spur and filum detethering were performed. The child had an uneventful recovery.

Complex split-cord malformations (complex SCMs) are SCMs associated with other intraspinal anomalies like lipomeningocele, myelomeningocele, neuroenteric cyst and/or tumors (e.g., dermoid or teratoma). [1] The association of dextrocardia with complex split-cord malformations is very rare and has been previously reported by us in the adult population. [2] This report illustrates the fact that preoperative MRI can be useful for surgical planning and management in children with apparently simple meningoceles.

 
   References Top

1.Ersahin Y, Barcin E, Mutluer S. Is meningocele really an isolated lesion? Childs Nerv Syst 2001;17:487-90.  Back to cited text no. 1  [PUBMED]  [FULLTEXT]
2.Dwarakanath S, Suri A, Garg A, Mahapatra AK, Mehta VS. Adult complex spinal dysraphism with situs inversus totalis: A rare association and review. Spine 2005;30:E225-8.  Back to cited text no. 2  [PUBMED]  [FULLTEXT]


    Figures

  [Figure - 1], [Figure - 2], [Figure - 3]


This article has been cited by
1 Split cord malformation A study of 300 cases at AIIMS 1990 2006
Mahapatra, A.K.
Journal of Pediatric Neurosciences. 2011; 6(3 SUPPL.): S41-S45
[Pubmed]



 

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