Journal of Pediatric Neurosciences
CASE REPORT
Year
: 2016  |  Volume : 11  |  Issue : 2  |  Page : 121--124

A case of primary spinal atypical teratoid/rhabdoid tumor in a 5-year-old child


Dipanker Singh Mankotia1, Vivek Tandon1, Bhawani Shankar Sharma1, Madhu Rajeshwari2, Mehar Chand Sharma2 
1 Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi, India
2 Department of Neuropathology, All India Institute of Medical Sciences, New Delhi, India

Correspondence Address:
Vivek Tandon
Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi
India

Atypical teratoid/rhabdoid tumor (AT/RT) is a rare central nervous system neoplasm affecting children, and isolated primary spinal involvement is extremely rare. Authors describe a case of spinal AT/RT in a 5-year-old male child presenting with rapidly progressing quadriparesis diagnosed and managed surgically and medically. Biopsy revealed large, rhabdoid cells with prominent nucleoli in nest and immunohistochemistry further showed loss of integrase integrator 1 expression considered to be gold standard for diagnosis. AT/RT has extremely poor prognosis with median survival being 6 months.


How to cite this article:
Mankotia DS, Tandon V, Sharma BS, Rajeshwari M, Sharma MC. A case of primary spinal atypical teratoid/rhabdoid tumor in a 5-year-old child.J Pediatr Neurosci 2016;11:121-124


How to cite this URL:
Mankotia DS, Tandon V, Sharma BS, Rajeshwari M, Sharma MC. A case of primary spinal atypical teratoid/rhabdoid tumor in a 5-year-old child. J Pediatr Neurosci [serial online] 2016 [cited 2019 Dec 9 ];11:121-124
Available from: http://www.pediatricneurosciences.com/article.asp?issn=1817-1745;year=2016;volume=11;issue=2;spage=121;epage=124;aulast=Mankotia;type=0