Journal of Pediatric Neurosciences
CASE REPORT
Year
: 2014  |  Volume : 9  |  Issue : 1  |  Page : 48--51

Desmoplastic infantile ganglioglioma: Report of an unusual case with a cranial defect


Recep Basaran1, Fatma Betul Cakir2, Nejat Isik3, Aydin Sav4, Ilhan Elmaci5 
1 Department of Neurosurgery, Dr. Lutfi Kirdar Training and Research Hospital, Istanbul, Turkey
2 Department of Pediatric Hematology-Oncology, School of Medicine, Bezmi Alem Foundation University, Istanbul, Turkey
3 Department of Neurosurgery, Goztepe Training and Research Hospital, Istanbul Medeniyet University, Istanbul, Turkey
4 Department of Pathology, School of Medicine, Acibadem University, Istanbul, Turkey
5 Department of Neurosurgery, School of Medicine, Medipol University, Istanbul, Turkey

Correspondence Address:
Recep Basaran
Department of Neurosurgery, Dr. Lutfi Kirdar Training and Research Hospital, Istanbul
Turkey

Desmoplastic infantile ganglioglioma (DIG) is a rare tumor that typically occurs in infants under the age of 24 months. These tumors commonly have a good prognosis after surgical resection despite their aggressive radiological appearances. Clinical signs are due to the large size of the tumor and include increased head circumference, bulging fontanel, sunset sign and seizures. We report an unusual DIG case who presented with parietal bulging associated with a bony defect. The patient was thought to have a leptomeningeal cystic formation, but on his cranial magnetic resonance imaging (MRI), we observed a centrally and homogeneously gadolinium-enhanced lesion fixed to the dura by its solid component. A surgical gross total resection was performed, and no residual tumor was observed on follow-up.


How to cite this article:
Basaran R, Cakir FB, Isik N, Sav A, Elmaci I. Desmoplastic infantile ganglioglioma: Report of an unusual case with a cranial defect.J Pediatr Neurosci 2014;9:48-51


How to cite this URL:
Basaran R, Cakir FB, Isik N, Sav A, Elmaci I. Desmoplastic infantile ganglioglioma: Report of an unusual case with a cranial defect. J Pediatr Neurosci [serial online] 2014 [cited 2020 Jul 3 ];9:48-51
Available from: http://www.pediatricneurosciences.com/article.asp?issn=1817-1745;year=2014;volume=9;issue=1;spage=48;epage=51;aulast=Basaran;type=0