Journal of Pediatric Neurosciences
CASE REPORT
Year
: 2014  |  Volume : 9  |  Issue : 1  |  Page : 39--41

Paroxysmal vascular events in Sturge– Weber syndrome: Role of aspirin


Jyoti Sanghvi, Sudhir Mehta, Swati Mulye 
 Department of Pediatrics, Sri Aurobindo Institute of Medical Sciences, Indore, Madhya Pradesh, India

Correspondence Address:
Sudhir Mehta
Department of Pediatrics, Sri Aurobindo Institute of Medical Sciences, Indore, Madhya Pradesh
India

Sturge-Weber syndrome (SWS) is a rare, sporadically occurring neurocutaneous disorder with a frequency of approximately 1 per 50,000. The hallmark is an intracranial leptomeningeal vascular angioma in association with a port wine nevus, usually involving ophthalmic or maxillary distribution of trigeminal nerve. Other clinical findings associated with SWS are seizures, glaucoma, hemiparesis and mental retardation. The radiological hallmark is DQTram-lineDQ or DQGyri-formDQ calcification. 25 to 56% of patients experience recurrent episodes of paroxysmal focal neurological deficits in form of transient hemiparesis, which may be due to vascular ischemia or postictal in origin. EEG helps to differentiate the exact etiology, as it is normal in former. Aspirin prophylaxis in those, due to ischemia decreases their recurrences and improves overall neurological prognosis. We report a 25-month-old child of SWS with recurrent episodes of transient hemiparesis and atypical midline location of facial vascular nevus.


How to cite this article:
Sanghvi J, Mehta S, Mulye S. Paroxysmal vascular events in Sturge– Weber syndrome: Role of aspirin.J Pediatr Neurosci 2014;9:39-41


How to cite this URL:
Sanghvi J, Mehta S, Mulye S. Paroxysmal vascular events in Sturge– Weber syndrome: Role of aspirin. J Pediatr Neurosci [serial online] 2014 [cited 2019 Jul 20 ];9:39-41
Available from: http://www.pediatricneurosciences.com/article.asp?issn=1817-1745;year=2014;volume=9;issue=1;spage=39;epage=41;aulast=Sanghvi;type=0