Journal of Pediatric Neurosciences
CASE REPORT
Year
: 2010  |  Volume : 5  |  Issue : 2  |  Page : 135--137

Split notochord syndrome associated with dorsal neuroenteric fistula: A rare entity


Punit Srivastava, AN Gangopadhyay, DK Gupta, SP Sharma 
 Department of Pediatric Surgery, IMS, BHU, Varanasi, Uttar Pradesh, India

Correspondence Address:
Punit Srivastava
Department of Pediatric Surgery, IMS, BHU, Varanasi 221005, Uttar Pradesh
India

Split notochord syndrome (SNS) is an extremely rare congenital malformation associated with anomalies of the vertebral column, gastrointestinal tract and central nervous system. Twenty cases of SNS associated with dorsal enteric fistula have been reported in literature till date. The present report describes a unique case of SNS associated with lumbosacral meningomyelocele, dorsal neuroenteric fistula and dorsal herniation of right kidney along with vessels. The neonate was well managed by excision of enteric fistula, closure of duramater of meningomyelocele and repair of posterior wall hernia after placement of kidney in renal fossa. This kind of entity is uncommon and not been reported earlier.


How to cite this article:
Srivastava P, Gangopadhyay A N, Gupta D K, Sharma S P. Split notochord syndrome associated with dorsal neuroenteric fistula: A rare entity.J Pediatr Neurosci 2010;5:135-137


How to cite this URL:
Srivastava P, Gangopadhyay A N, Gupta D K, Sharma S P. Split notochord syndrome associated with dorsal neuroenteric fistula: A rare entity. J Pediatr Neurosci [serial online] 2010 [cited 2019 Jul 16 ];5:135-137
Available from: http://www.pediatricneurosciences.com/article.asp?issn=1817-1745;year=2010;volume=5;issue=2;spage=135;epage=137;aulast=Srivastava;type=0