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LETTER TO THE EDITOR
Year : 2016  |  Volume : 11  |  Issue : 2  |  Page : 163
 

Disseminated spinal lymphangiomatosis


Department of Neurosurgery, Arad Hospital, Tehran, Iran

Date of Web Publication3-Aug-2016

Correspondence Address:
Mahmoud Reza Khalatbari
Somayeh Street, Between Dr. Shariati and Bahar Avenue, 1445613131, Tehran
Iran
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/1817-1745.187654

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How to cite this article:
Khalatbari MR, Moharamzad Y. Disseminated spinal lymphangiomatosis. J Pediatr Neurosci 2016;11:163

How to cite this URL:
Khalatbari MR, Moharamzad Y. Disseminated spinal lymphangiomatosis. J Pediatr Neurosci [serial online] 2016 [cited 2019 Nov 15];11:163. Available from: http://www.pediatricneurosciences.com/text.asp?2016/11/2/163/187654


Dear Sir,

A 17-year-old patient presented complaining of low back pain of 2 years duration which aggravated in the past 6 months. This was accompanied by bilateral pins and needles sensations over his lower extremities as well as worsening shortness of breath. Spinal magnetic resonance imaging (MRI) showed extensive hyperintense lesions of all lumbar vertebral bodies, bilateral sacrum and iliac as well as prevertebral areas and the retroperitoneum [Figure 1]. The lesions were hyperintense on both T1- [Figure 2]a and T2-weighted [Figure 2]b images. On the chest computed tomography (CT) scan, diffuse right-sided chylothorax associated with mediastinal shift was detected [Figure 3]. Histopathological examination of the vertebral bodies and iliac crest biopsy samples revealed extensive lymphangiomatosis. This is a congenital benign condition of the lymphatic system proliferation which can affect osseous and visceral organs and usually diagnosed before age of 20 years. [1] It has been advocated that MRI should be obtained in the assessment of this condition owing to its superiority to CT scan. [2] In this patient, a pleuroperitoneal shunt was inserted. On the last follow-up, he was in good general condition with no complaint.
Figure 1: (a) Sagittal T2-weighted spinal magnetic resonance imaging shows hyperintense lesions of the lumbar vertebral body and spinous processes. (b) Sagittal T1-weighted magnetic resonance imaging of the lumbar spine shows mixed hyper- and hypo-intense lesions of the vertebral bodies and spinous processes. (c) Coronal T2-weighted magnetic resonance imaging of the lumbar spine shows hyperintense lesions of the vertebral bodies

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Figure 2: (a) Axial T1-weighted magnetic resonance imaging of the lumbar spine shows hyperintense lesions of the vertebral body and paravertebral tissues and retroperitoneum. (b) Axial T2-weighted magnetic resonance imaging of the lumbar spine shows hyperintense lesion of the vertebral body

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Figure 3: Axial computed tomography scan of the chest shows massive right chylothorax with mediastinal shift

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   References Top

1.
Ozturk A, Yousem DM. Magnetic resonance imaging findings in diffuse lymphangiomatosis: Neuroradiological manifestations. Acta Radiol 2007;48:560-4.  Back to cited text no. 1
    
2.
Renjen P, Kovanlikaya A, Narula N, Brill PW. Importance of MRI in the diagnosis of vertebral involvement in generalized cystic lymphangiomatosis. Skeletal Radiol 2014;43:1633-8.  Back to cited text no. 2
    


    Figures

  [Figure 1], [Figure 2], [Figure 3]



 

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